Androgen Insensitivity syndrome
Background
Androgen Insensitivity syndrome: Complete Androgen Insensitivity syndrome (CAIS); Partial Androgen Insensitivity syndrome (PAIS); Androgen Resistance syndrome; Testicular Feminisation syndrome; Feminising Testes syndrome; Male Pseudo-Hermaphroditism; Goldberg-Maxwell syndrome (CAIS); Morris's syndrome (CAIS); Lub's syndrome (PAIS); Reifenstein syndrome (PAIS); Gilbert-Dreyfus syndrome (PAIS)
Normally, humans have twenty-three pairs of chromosomes. On fertilisation, the chromosomes combine to give a total of forty-six (twenty-three pairs). A female usually has an XX pair of sex chromosomes and a man an XY pair. The female affected by androgen insensitivity syndrome (AIS) has an XY pair of sex chromosomes.