Degos disease
Background
Degos disease: Malignant Atrophic Papulosis: Kohlmeier-Degos disease
Degos disease is a rare inherited condition first described by Kohlmeier in 1941 and Degos in 1942. There are thought to have been about one hundred and fifty cases of the condition reported in medical literature. The most severe form is Systemic Degos disease affecting children and adolescents with most cases occurring in young adults. Benign Degos disease also affects adults.