Hirschsprung's disease
Background
Hirschsprung disease: Hirschsprung's disease; Aganglionosis
Hirschsprung's disease (HD) affects 1 in 4,500 live births throughout the world. In the United Kingdom this equates to about one hundred and fifty to two hundred new cases of HD each year.
HD affects the nerves of the large intestine (colon). The main function of the colon is to conserve water and salt, to store faecal material (stool), and to regulate its release from the body. Normally, special nerve cells (ganglion cells) control the pushing movement of muscles in the colon and push stool to the anus where it is expelled from the body.