Dancing Eye syndrome
How is it treated?
The treatments used have been those used to suppress the immune response. Steroids given by mouth or injection have been the main drugs used. More recently, intra-venous immunoglobulin infusions have been used with benefit either instead of, or in addition to, steroids. Other treatments which may help include azathioprine, cyclophosphamide, plasma exchange and rituximab. Because the condition is very rare and variable in the way it develops, it has been very difficult to collect enough children to formally evaluate different treatment options in a controlled and scientific fashion. Currently such a study is under way in the USA but will probably take some time to reach a conclusion.
The longer term outcome of this condition is very variable. Occasional children fully recover very quickly without treatment. Others respond to treatment partially or completely. Some of these children may relapse either as the treatment is withdrawn or following a viral infection which may have stimulated the immune response. More severely affected children often have longer-term problems with learning, co-ordination, behaviour and sleep.
What are the causes?
| Inheritance patterns and prenatal diagnosis ![]()