Ectodermal Dysplasia
What are the symptoms?
Each syndrome usually involves a different combination of symptoms, which can range from mild to severe, such as:
- Absence or abnormality of hair growth;
- Absence or malformation of some or all teeth;
- Inability to perspire, which causes overheating;
- Abnormalities of the nails - which may be brittle and grow slowly or be thickened or ridged;
- Frequent infections due to immune system deficiencies or, in some cases, the inability of cracked or eroded skin to keep out disease-causing bacteria;
- Absence or malformation of some fingers or toes;
- Cleft lip and/or palate;
- Irregular skin pigmentation.
In addition to the above they may have:
- Sensitivity to light;
- Respiratory infections and allergies;
- A lack of breast development;
- Impairment or loss of hearing or vision;
- Constipation;
- A host of other challenges.
Individuals affected by ED face a lifetime of special needs which may include:
- Dentures at a young age with frequent adjustments and replacements;
- Special diets to meet dental/nutritional needs;
- Air conditioned environments;
- Wigs to conceal hair and scalp conditions;
- Genetic testing to confirm the precise diagnosis and identify carriers;
- Protective devices from direct sunlight;
- Osseointegrated dental implants;
- Respiratory therapies.
Background
| Eye problems and ectodermal dysplasia 
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