Facioscapulohumeral Muscular Dystrophy
What are the causes?
Normally, at a particular site on the gene map (region '4q35' at one end of chromosome 4), each of us has many copies of a particular sequence of genetic instruction (DNA). In most cases, FSHD is caused when the number of copies is reduced below a certain level on one of the pair of chromosome 4's. This seems to affect the way that DNA in that region is packed into the chromosome, and may well be triggering the production or assembly of some proteins which would not normally be made in muscle. The effect is to cause damage to the muscle cells.
What are the symptoms?
| How is it treated? ![]()