Incontinentia Pigmenti
What are the symptoms?
The hallmark features of IP appear on the skin:
- In the first months of life, abnormal redness of the skin followed by lines of blisters in all areas except the face;
- As the blisters heal, warty areas occur on the skin of the hands and feet. In most cases these clear by six months of age;
- Hyperpigmented (excessive brown pigmentation) streaks or whorls occurring mainly on the trunk but which fade in adolescence. These give IP its name;
- From adolescence into adulthood, pale hairless streaks or patches.
Other features of IP include:
- Absent, small or misshapen teeth;
- Alopecia (baldness) or coarse, wiry dull hair;
- Ridging or pitting of the nails;
- Excessive formation of blood vessels in the retina of the eye.
Occasionally, seizures and learning disability occur. Life expectancy is normal.
Background
| What are the causes? 
Tell us what you think of this information...
Print whole article
|
|
|
|
Donate Now
makingcontact.org
Pounds for parents
Subscribe to the